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Center for Cardiovascular Genetics | University Hospitals …

The Center for Cardiovascular Genetics at University Hospitals Harrington Heart & Vascular Institute specializes in evaluation, treatment, diagnosis and genetic counseling for individuals of all ages and their family members. The goal of the Center for Cardiovascular Genetics is to identify and treat patients with inherited cardiac conditions, those at risk of developing an inherited cardiac condition, and those who are at risk for sudden cardiac death.

Although many cardiac conditions result from diet, smoking, lack of exercise, high cholesterol, or other medical conditions such as diabetes, some cardiac conditions are the result of a genetic abnormality. These genetic abnormalities can result in problems with the hearts muscle function (cardiomyopathy) or problems with the hearts electrical system, which may put patients at risk for sudden cardiac death.

A genetic abnormality can be inherited and passed down through families. Family members with the same genetic abnormality may present with a variable degree of symptoms. Some patients may have no symptoms and others will have significant symptoms.

Inherited cardiac conditions which may put patients at risk for sudden cardiac death or arrest (SCD/A) include:

Comprising physicians specializing in cardiomyopathy, congestive heart failure, cardiac electrophysiology, medical genetics and a certified genetic counselor, the Center for Cardiovascular Genetics is designed to identify patients with inherited conditions or genetically determined cardiac disease. Diagnosis of an inherited condition can be made using a combination of cardiac and genetic testing.

Consultation with a medical geneticist and certified genetic counselor may be recommended to determine if genetic testing will aid in the diagnosis, direct treatment strategy, and identify other at-risk or affected family members.

As an outpatient clinic, patients may meet and be evaluated by an electrophysiologist (a doctor specializing in heart rhythm disorders), a cardiologist specializing in cardiomyopathy, and a registered nurse.

Cardiac evaluation will include a thorough history and physical examination. Sometimes additional testing may be recommended in order to establish the patients diagnosis or risk. This may include one or more of the following:

Once a diagnosis is made, the patient will meet with the medical geneticist and the genetic counselor to discuss whether genetic testing would benefit them or other members of their family. Genetic testing is done by providing a sample of blood that will be sent to a laboratory where the genetic material will be examined. The genetic analysis will look for abnormal changes in genetic information that are responsible for the inherited cardiac disease.

Once the genetic testing is complete, the patient will return to the Center for Cardiovascular Genetics where the genetic results will be discussed with the geneticist and the genetic counselor. They will explain what the findings mean for the patient and his or her family members. They can also help patients discuss this information with other family members.

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Center for Cardiovascular Genetics | University Hospitals ...

Embryology Synonyms, Embryology Antonyms | Thesaurus.com

We cannot pursue the mind into embryology: we can only trace how, after birth, it begins to grow.

See further the same author's article "Embryology" in the Ency.

This comparison I have been able to make from a study of the embryology of Isotoma.

Is there any fallacy in speaking of the Embryology of the New Life?

But that belongs to the domain of Embryology, which is a separate science.

He is not only a master of zoology, but has a good command of botany and embryology.

The same holds good with the evidence from Embryology and from Palontology.

Until then embryology had been regarded as a purely descriptive science.

The embryology of Blatta germanica and Doryphora decimlineata.

The whole of embryology, in every department, is made up of examples of the same law.

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Embryology Synonyms, Embryology Antonyms | Thesaurus.com

Anatomy & Physiology Quizzes & Games – Kenhub

Anatomy - want to learn more about it?

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I would honestly say that Kenhub cut my study time in half.Read more.Kim Bengochea, Regis University, Denver

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Anatomy & Physiology Quizzes & Games - Kenhub

Biochemistry, B.S. < Temple University

Learn more about the Bachelor of Science in Biochemistry.

The Bachelor of Science degree in Biochemistry prepares students for excellence in graduate or medical school, and employment in the chemical, biotechnological, or pharmaceutical industries. Students learn a wide array of topics in Biology, Chemistry, Mathematics, and Physics. In upper division studies, Biochemistry majors learn to apply biochemical principles to real-life situations via problem-based approaches in their courses. Laboratory courses give students the tools they will need as biochemists to pursue research. Accomplished majors are encouraged to pursue independent research with a professor, and to present their work internally and at national meetings.

Undergraduate Contact Information:

Dr. Robert Sanders, ChairBiology-Life Sciences Building, Room 255215-204-8851

Dr. Dan Strongin, Chemistry ChairBeury Hall, Room 130215-204-7118

Dr. Angela Bricker, Faculty Advisor, BiologyBiology-Life Sciences Building, Room 248C215-204-8578abricker@temple.edu

Dr. Steven Fleming, Faculty Advisor (Last names A-C), ChemistryBeury Hall, Room 344215-204-0359sfleming@temple.edu

Dr. Roy Keyer, Faculty Advisor (Last names D-G), ChemistryBeury Hall, Room 440215-204-7286roy.keyer@temple.edu

Dr. Spiridoula Matsika, Faculty Advisor (Last names H-K), ChemistryBeury Hall, Room 242215-204-7703spiridoula.matsika@temple.edu

Dr. Andrew Price, Faculty Advisor (Last names L-M), ChemistryBeury Hall, Room 222C215-204-1048acprice@temple.edu

Dr. Vince Voelz, Faculty Advisor (Last names N-R), ChemistryBeury Hall, Room 240215-204-1973vincent.voelz@temple.edu

Dr. Vladi Wilent, Faculty Advisor (Last names S-T), ChemistryBeury Hall, Room 440215-204-7186vladi.wilent@temple.edu

Dr. Michael Zdilla, Faculty Advisor (Last names U-Z), ChemistrySERC, Room 656215-204-7886michael.zdilla@temple.eduNote: Due to restricted access to the 6th floor of SERC, please email Dr. Zdilla to set up an appointment.

Note: A grade of C or higher in CHEM1031 or its Honors alternate is required to take BIOL1111. Grades of C or higher in both CHEM1031 and CHEM1032 or their Honors alternates are required to take BIOL2112. Grades of C or higher in BIOL1111 and BIOL2112 or their Honors alternates are required to take upper-level Biology courses, and a C- or higher is required unless otherwise specified in all other courses for the major, including course prerequisites. Most research and Independent Study courses are not available for major credit, such as:

Courses listed under the major requirements for the degree will be included in the calculation of the major GPA. Courses that could not apply toward the major as an elective or required course would not be counted in the calculation of the major GPA. This would include BIOL1011, for example.

To graduate with Distinction in Major, students are required to achieve a 3.33 GPA or higher in all the Biology and Chemistry courses in their major.

All prospective majors should schedule an appointment with one of the departmental advisors (names of current Faculty Advisors are available in the About section) to plan a program of study. The recommended order of courses for the major is listed below; a different order is acceptable as long as the student adheres to prerequisite requirements.

Students are required to take two advanced biochemistry electives from the following list:

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Biochemistry, B.S. < Temple University

Genetics | Time

After a scientist claimed that he had produced the first human babies born ...

After a scientist claimed that he had produced the first human babies born after editing their genomes with a new technique called CRISPR, his university is investigating his report

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Genetics | Time

Diverse Lineages of Candida albicans Live on … – genetics.org

THE yeast Candida albicans is the most common yeast pathogen in humans (Barnett 2008), yet it is also a commensal in most humans and inhabits a broad range of warm-blooded animals (Barnett 2008). Unlike other Candida species, C. albicans is only rarely isolated from plants or other environmental substrates (Barnett 2008; Lachance et al. 2011) and is generally considered an obligate commensal (Hall and Noverr 2017). There were early discoveries of C. albicans on gorse flowers and myrtle leaves on a hillside grazed by sheep and goats in Portugal (van Uden et al. 1956), and on grass in a pasture in New Zealand (Di Menna 1958). More recently it was isolated from a beetle and an African tulip tree in the Cook Islands (Lachance et al. 2011), and we isolated C. albicans from oak trees in an ancient wood pasture in the United Kingdom (Robinson et al. 2016).

Many species of yeast live on trees, including other opportunistic pathogenic Candida species such as Candida tropicalis and Candida parapsilosis (Maganti et al. 2011; Carvalho et al. 2014). Genetic data shows that Saccharomyces cerevisiae, which can also infect humans, stably persists in wild woodland habitats (Fay and Benavides 2005; Aa et al. 2006), and the high genomic diversity of S. cerevisiae from Asia shows that forests are its ancestral habitat (Peter et al. 2018). Indeed, woodlands probably represent the ancestral habitat for all Saccharomyces species (Eberlein et al. 2015). Forests may also be an ancestral habitat and reservoir for other human fungal pathogens such as Cryptococcus neoformans and Cryptococcus gattii (May et al. 2016; Gerstein and Nielsen 2017).

The isolation of C. albicans from plants (van Uden et al. 1956; Di Menna 1958; Lachance et al. 2011; Robinson et al. 2016) raises the question of whether C. albicans is truly an obligate commensal of warm-blooded animals. Laboratory experiments show that C. albicans can grow and mate at room temperature (Hull et al. 2000; Magee and Magee 2000;), and it retains an intact aquaporin gene whose only known phenotype is freeze tolerance (Tanghe et al. 2005). It is therefore possible that C. albicans populations could survive away from warm-blooded animals.

Here, we generated genome sequences for three strains of C. albicans from oak bark from the New Forest in the United Kingdom (Robinson et al. 2016). These are the first C. albicans genomes sequenced from a nonanimal source, and we compared them to the genomes of over 200 strains from humans and animals (Muzzey et al. 2013; Hirakawa et al. 2015; Ropars et al. 2018). Although they were collected from the same woodland, these oak strain genomes are genetically diverged from one another, and are more similar to diverged clinical lineages than they are to each other. However, oak strains differ from clinical strains in showing higher levels of genome-wide heterozygosity, suggesting that they were subject to different selection or mutation pressures. The genetic diversity of C. albicans in this woodland implies that they have lived there long enough for distinct lineages to accumulate on unusually old trees. Therefore, C. albicans can live in the oak environment for prolonged periods.

We generated short-read genome data for the type strain of C. albicans (NCYC 597) and three strains of C. albicans from the bark of oak trees in the New Forest in the United Kingdom (Robinson et al. 2016; Table 1). Robinson et al. (2016) describe the methods used to isolate the oak strains. Negative controls were generated at every field site, and these were subjected to the same procedures and handling as other samples except that no bark was inserted into negative controls after opening tubes in the field. Two of the three trees with C. albicans (FRI5 and FRI10) were directly associated with negative controls and there were negative controls at 6 of the 30 trees sampled in the New Forest (FRI5, FRI10, FRI15, OCK5, OCK10, and OCK15). In total, six out of the 125 sample tubes collected in the New Forest (Robinson et al. 2016) were negative controls and all of them were clear.

The type strain of C. albicans (NCYC 597) and the three oak strains were characterized biochemically, morphologically, and physiologically according to the standard methods described by Kurtzman et al. (2011) (Supplemental Material, Table S1).

We used the reference genome sequence for C. albicans strain SC5314_A22 (haplotype A, version 22; GCF_000182965.3) from the NCBI reference sequence database. For comparisons of oak strain to clinical strain genomes, we used short-read genome data from the European Nucleotide Archive (ENA) for wild-type SC5314 (SRR850113) and the related 1AA mutant (strain AF9318-1, SRR850115; Legrand et al. 2008; Muzzey et al. 2013), 20 clinical strains (PRJNA193498; Hirakawa et al. 2015) (Table S2), and 182 clinical strains (PRJNA432884; Ropars et al. 2018) (Table S3).

Purified genomic DNA was extracted from a 10 ml culture, in a 1.5 ml initial suspension using a MasterPure yeast DNA purification kit (Epicentre) and following the manufacturers instructions. Whole-genome sequencing of four C. albicans genomic DNA samples (NCYC 4144, NCYC 4145, NCYC 4146, and NCYC 597) was carried out at the Earlham Institute (Norwich, UK). Libraries were constructed using their Low Input Transposase-Enabled (LITE) methodology for library construction of small eukaryotic genomes based on the Illumina Nextera kits. Each library pool was sequenced with a 2 250 bp read metric over six lanes of an Illumina HiSeq2500 sequencer. Adapters were trimmed using Trimmomatic (version 0.33; Bolger et al. 2014) with default settings for paired-end data and the ILLUMINACLIP tool (2:30:10). We used FastQC (version 0.11.4; http://www.bioinformatics.babraham.ac.uk/projects/fastqc/) to check read quality and the presence of adapters before and after trimming, and used trimmed, paired-read data in subsequent analyses.

Short-read data for all strains [three oak strains, the type strain, 182 strains from Ropars et al. (2018), 20 clinical strains from Hirakawa et al. (2015), SC5314 and the 1AA mutant from Muzzey et al. (2013)] were mapped to the SC5314_A22 reference genome using BurrowsWheeler Aligner (bwa mem, version 0.7.10; Li and Durbin 2009). We used SAMtools (version 1.2; Li et al. 2009) to generate sorted bam files that were merged in cases where there were multiple sets of read-pair data files per strain. To generate a consensus (in genomic variant call format, gVCF) we used mpileup from SAMtools and then bcftools call (with the -c option). SAMtools mpileup was used with default settings except that maximum read depth was increased to 10,000 reads and we used the -I option so insertions and deletions were excluded.

To estimate levels of heterozygosity either genome-wide (Table 2) or in 100 kb nonoverlapping windows (Figure 1B), we estimated the proportion of sites that were heterozygous. For all estimates of levels of heterozygosity, only high-quality sites (phred-scaled quality > 40) were considered. Sites were considered heterozygous if the proportion of sites differing from the reference sequence (the allele ratio) was between 0.2 and 0.8. In a diploid, it is also possible for sites to be heterozygous with an allele ratio of 1.0 in cases where three alleles exist for a site because both alleles could differ from that of the reference genome. For example, the reference genome may have an A at a site, and a study strain could show an allele ratio of 1.0 while being heterozygous for C and T alleles. However, levels of intraspecific genetic diversity are sufficiently low that we expect triallelic sites to represent a small proportion of all heterozygous sites, and therefore not to affect our conclusions. If the true proportion of heterozygous sites is 0.007 (close to the levels we observe in Table 2), then the expected proportion of sites with a second point substitution would be (i.e., 0.0072). The observed number of high-quality triallelic sites in each (14 Mbp) genome sequence are slightly lower than expected: up to (144 sites) for the oak strains and all clinical strains except the type strain. The type strain (NCYC 597), which is mostly triploid, has the largest number of triallelic sites (173 sites). Differences between oak and clinical strains in the exclusion of these few sites cannot explain the higher levels of heterozygosity seen for oak strains. exceeding that of clinical strains by thousands of sites.

C. albicans from oak are mostly diploid with some loss of heterozygosity (LOH). A. The proportion of base calls differing from the reference strain (allele ratios) are mostly 1.0 or 0.5 for oak strains (NCYC 4144-6), suggesting diploidy. Regions that recently homozygozed are shaded light blue. The points that occur in these LOH regions often correspond to the locations of known repeats where short reads are probably mismapped. The oak strain with at its mating locus (NCYC 4144) arrived at this state by LOH for the whole of chromosome 5. B. The proportion of heterozygous sites in 100 kb nonoverlapping windows are either high or low for oak strains (NCYC 4144, NCYC 4145, and NCYC 4146). For oak strains (shown here) and clinical strains (Figure S2) we see two modes; heterozygosity is either low (below the red line at 0.1%), or high (with a mean > 0.4%). Regions with >0.1% heterozygous sites in a 100 kb window were classed as LOH regions and are shown in light blue in A.

Using seqtk from SAMtools, we converted base calls in gVCF format to fasta format sequence and filtered bases that had quality scores below a phred-scaled quality score of 40 (equivalent to an error rate of 1 in 10,000). All genome sequences were mapped against the reference genome, and were therefore already aligned against it because insertions and deletions were excluded. fasta format alignment files were converted to phylip format using fa2phylip.pl (Bensasson 2018b).

We inferred the genotype calls at multilocus sequence typing (MLST), mating type-like (MTL), and ribosomal DNA (rDNA) loci for the type strain and the three oak strains using the genomic data generated above, and also verified these by independent DNA extraction, PCR, and sequencing. Purified genomic DNA was extracted as above, except that 100 units of lyticase was used to degrade the fungal cell wall for each preparation before DNA extraction. The DNA yield from each preparation was determined by fluorimetry using a Qubit 3.0 fluorometer (Thermo Fisher). The seven housekeeping MLST genes (AAT1, ACC1, ADP1, MPI1b, SYA1, VPS13, and ZWF1b) used routinely for C. albicans strain typing were PCR-amplified and sequenced following the standard protocol (Bougnoux et al. 2003; Tavanti et al. 2003). The C. albicans MLST database (https://pubmlst.org/calbicans/) was used to determine allele identity (sequence type, ST). The mating type ( or ) was determined by PCR using the method described by Tavanti et al. (2003). The complete internal transcribed spacer (ITS) region, encompassing ITS1, the 5.8S rRNA gene, and ITS2, was PCR-amplified directly from whole-yeast cell suspensions following the procedure and PCR parameters as described by James et al. (1996). The ITS region was amplified and sequenced using the conserved fungal primers ITS5 and ITS4 (White et al. 1990).

We developed a Perl script, vcf2allelePlot.pl (Bensasson 2018b), that uses R to visualize all the base calls that differ between a strain and the reference genome (SC5314_A22; Figure 1A and Figure S1). This vcf2allelePlot.pl was also used to identify loss of heterozygosity (LOH) regions as follows. The genome was divided into 100 kb nonoverlapping windows and LOH was called for windows where the proportion of heterozygous sites was <0.1%. We estimated the proportion of heterozygous sites after excluding low quality sites (phred-scaled consensus quality < 40), centromeres, annotated repeats, and sites in each window with over double the average genome-wide read depth for a strain. A large window size (100 kb) minimizes the chances of excluding a region of low heterozygosity due to sampling error. For example, for strains with 0.2% mean heterozygosity (Table 2), we expect around half the 10 kb windows to have <20 heterozygous sites per 10 kb region. Using a 100 kb window a random sample with 0.2% heterozygosity (expected 200 heterozygous sites), is less likely to dip below 0.1% (100 heterozygous sites). We used histograms generated in R (version 3.2.3 for this and all other statistical analysis) to decide the 0.1% threshold for the identification of LOH regions (Figure 1B and Figure S2).

For a comparison of heterozygosity among the clades defined by Ropars et al. (2018) for their clinical C. albicans strains, we used a standard analysis of variance with the lm function in R, and clade set as a factor with 18 levels (one level for each of the 17 defined clades and another level for strains of unknown clade). We tested whether oak strains (NCYC 4146, NCYC 4144, and NCYC 4145) showed higher heterozygosity than expected for their clade assignment (clades 4, 18, and unknown), by including oak as a separate clade level, and comparing this to a model where oaks were simply defined according to their clade. All models were checked using the model-checking plots of R as recommended in Crawley (2012). In addition, we used histograms to verify that heterozygosity levels were approximaetely normally distributed around the mean for all clades where at least 10 strains were available: clades 1, 2, 3, 4, 11, 13, and strains from unknown clades.

We determined the relationships between strains using a maximum likelihood phylogenetic approach. For the phylogenetic analysis of the genome data from Ropars et al. (2018) shown in Figure 2A, we randomly selected three strains to represent clades where more than 3 strains were available, used all available strains for other clades and included the data for the three oak strains, the type strain (NCYC 597) and SC5314 (Muzzey et al. 2013). For all strains, genome sequence was generated by aligning each read to the SC5314 haplotype A reference while excluding all insertions (see above). Therefore all genome sequences were already aligned to this reference, and there was no need for further alignment. The resulting alignments for each chromosome are available from Bensasson (2018a). All eight chromosomes were concatenated into a single 14,282,655 bp genome-wide alignment using alcat.pl (Bensasson 2018b), which included 313,250 variable sites that included at least one homozygous difference between strains. We used the maximum likelihood phylogenetic approach implemented in RAxML (version 8.1.20; Stamatakis 2014) with a general time reversible evolutionary model, a -distribution to estimate heterogeneity in base substitution rates among sites (GTRGAMMA) and 100 bootstrap replicates. RAxML treats heterozygous base calls as missing data, so the resulting phylogeny is based on homozygous differences between strains.

C. albicans from oak are more similar to clinical strains than to each other. Phylogenetic and pairwise sequence comparisons show that the oak strain NCYC 4146 is similar to clade 4 clinical strains, NCYC 4144 is similar to clade 18 clinical strains, and NCYC 4145 is diverged from the 17 clades sampled and 10 further strains of unknown clade. A. Genome-wide phylogeny. Maximum likelihood phylogenetic analysis of a whole-genome alignment (14,282,655 bp) shows that oak strains (green) are more closely related to clinical strains than they are too each other. Bootstrap support is estimated from 100 replicates and only values >70% are shown. The alignment contained 313,250 variable sites with at least one homozygous difference between strains. B. Painted chromosomes of oak strains. Most parts of the genomes of oak strains are more similar to clinical strains than to other oak strains (green). The genome of each oak strain was colored according to the clade assignment of the most similar strain for each 100 kb window in the genome using the colours for each clade shown in A. Regions are colored white if a strain sequence is diverged from all the other oak or clinical strains that we sampled (the proportion of sites differing is >0.028%). From left to right, NCYC 4146 in light blue is most similar to Clade 4 strains, NCYC 4144 in blue is most similar to Clade 18, and NCYC 4145 is mostly white and therefore diverged from all known clades.

To test whether a strain is similar to a single clade in all parts of its genome, we developed faChrompaint.pl (Bensasson 2018b) to paint chromosomes according to similarity to known clades. Several other tools already exist for painting chromosomes in silico to identify admixture between populations [reviewed in Schraiber and Akey (2015)]; however, these require phased haplotype data, which are not available for C. albicans. The faChrompaint.pl script takes fasta formatted whole-chromosome alignments as input, and divides the genome of a study strain into nonoverlapping windows (we set the window size to 100 kb). The script uses R to generate a plot with every window colored according to the clade assignment of the most similar strain in that window. The most similar DNA sequence was the one with the lowest proportion of differing sites. We defined clades using the clade assignments made by Ropars et al. (2018) for the strains confirmed in our phylogenetic analysis (Figure 2A), and colored windows green if their greatest similarity was to an oak strain sequence. If a strain shows high genetic divergence from all other strains, then similarity to a known clade does not necessarily imply recent common ancestry. We therefore filtered diverged regions by leaving those windows blank. More specifically, we did not color windows with over 0.028% divergence from known clades because most within-clade pairwise comparisons (90%) show divergence levels <0.028%, whereas most between-clade comparisons show divergence >0.028% (Figure S3).

We recently discovered C. albicans living on the bark of oak trees in a wood pasture in the New Forest (Table 1; Robinson et al. 2016). The three strains we isolated are available from the NCYC (NCYC 4144, NCYC 4145, and NCYC 4146). For several reasons, the data from Robinson et al. (2016) suggest that these three oak strains represent independent isolates and not laboratory contaminants or recent migrants from a single human or animal source. First, bark samples were collected into tubes using sterile technique from heights of at least 1.5 m above the ground, thus reducing the chances of direct contamination from animal manure. Second, we generated negative controls at the time of bark collection for two out of the three trees with C. albicans and they gave rise to no colonies after enrichment culturing. Subsequent DNA extraction and PCR amplification from these control plates were all also blank (Robinson et al. 2016). Third, the three trees harboring C. albicans were between 73 and 150 m apart, therefore any migration from animal manure or from humans to tree bark would have to occur in three separate events. Finally, trees with C. albicans had larger trunk girths and therefore were older than most of the 112 uncoppiced trees sampled across Europe [data from Robinson et al. (2016); Wilcoxon test, ] or in the New Forest (Table 1; Wilcoxon test, ). There is no reason to expect a greater level of migration from animals on old trees unless C. albicans are able to live on oak for many years.

C. albicans that were isolated from plants in the past were pathogenic in mammals, but did not differ from each other phenotypically (van Uden et al. 1956; Di Menna 1958). To test whether the C. albicans strains from oak also resembled each other phenotypically, we tested the growth of oak strains under the standard conditions described in Kurtzman et al. (2011). All three oak strains were able to grow at elevated temperatures (3742; Table S1), suggesting that they would be able to survive temperatures in a mammalian host. The oak strains also produced well-formed, irregularly branched pseudohyphae when grown on either corn meal agar or potato dextrose agar, and grew in 60% glucose, showing that they were highly osmotolerant. The phenotypes of the three oak strains differed from each other in that NCYC 4145 and NCYC 4146 displayed salt tolerance by growing in the presence of 10% NaCl, but NCYC 4144 did not (Table S1). The results of further growth tests on agar, in broth, and under other conditions were as previously described for C. albicans (Lachance et al. 2011), with the exception that one oak strain (NCYC 4144) formed pseudohyphae in YM broth and did not grow on soluble starch (Table S1).

In addition, the three C. albicans strains from oak must be able to survive the cool temperatures and other characteristics of the oak environment because they lived there until they were isolated from bark. They also survived enrichment, storage, and culturing conditions, which include growth at room temperature (30) in a liquid medium containing chloramphenicol (1 mg/liter) and 7.6% ethanol, on selective plates with a sole carbon source of methyl--D-glucopyranoside (Sniegowski et al. 2002), storage at 4, and as 15% glycerol stocks at 80 (Robinson et al. 2016).

Clinical strains of C. albicans are predominantly diploid (Hickman et al. 2013; Hirakawa et al. 2015), yet aneuploidy is often observed and may be an important mechanism for adaptation (Li et al. 2015; Todd et al. 2017). In addition, clinical strains undergo LOH with even greater frequency than changes in aneuploidy (Ford et al. 2015; Ropars et al. 2018), and LOH can affect mating type and other phenotypes (Bougnoux et al. 2008; Forche et al. 2011; Ford et al. 2015; Hirakawa et al. 2015). We therefore tested for aneuploidy and LOH in oak strains using a standard base calling approach for estimating ploidy and LOH from genome sequence, and validated our methods by using them to identify known aneuploidy and LOH events in clinical and laboratory strains (Supplemental Results).

The base calling approach we used (the B allele approach; Teo et al. 2012; Yoshida et al. 2013; Zhu et al. 2016) estimates the minimum ploidy of a yeast strain by examining the base calls of short read genome data mapped to a reference genome (SC5314 haplotype A). In a haploid genome or a homozygous diploid, base calls at the single nucleotide polymorphic (SNP) sites relative to the reference genome will all differ from the reference genome, so the proportion of base calls that differ from the reference will be approximately equal to 1 (e.g., chromosome 5 of the oak strain NCYC 4144 in Figure 1A). In a diploid, the proportion of base calls differing from the reference will be approximately equal to 1 at homozygous SNP sites or 0.5 at heterozygous SNP sites (e.g., the oak strain NCYC 4146 in Figure 1A). In triploids, the proportion of calls differing from the reference will be 0.66 and 0.33 at heterozygous sites (e.g., chromosome R of NCYC 4144 in Figure 1A) and so on. It is also possible to detect aneuploidy by comparing read depth between chromosomes. However, we use a base calling approach because read depth approaches are sensitive to biases when genomes are fragmented enzymatically (Marine et al. 2011; Quail et al. 2012; Teo et al. 2012), as they were in this study (see Materials and Methods).

For all three oak strains, the proportion of base calls differing from the reference is 0.5 at most heterozygous sites and therefore they are predominantly diploid (Figure 1A). NCYC 4146 appears to be euploid, but NCYC 4144 and NCYC 4145 show evidence of trisomy on chromosome R. The type strain and some other clinical strains are also trisomic for chromosome R or have three copies of its right arm (Hirakawa et al. 2015; Ropars et al. 2018; Figure S1). The right arm of chromosome R may therefore exist in three copies with appreciable frequency in natural strains of C. albicans. Trisomy of chromosome R can result in slow growth in the laboratory (Hickman et al. 2015), and has been associated with resistance to triazoles (Li et al. 2015).

The oak strains also showed several chromosomal segments (light blue in Figure 1A) that were homozygous (heterozygosity < 0.1% in Figure 1B). Read depth in regions with low heterozygosity is similar to that in the rest of the genome (Figure S4), therefore these regions do not represent deletions or the loss of a chromosome. They are regions that have undergone recent LOH. Consistent with the proposal that aneuploidy persists for less time in C. albicans populations than LOH regions (Ford et al. 2015), we observe a greater number of LOH regions than aneuploidy events for every oak and clinical strain (Figure 1 and Figure S1).

One oak strain (NCYC4144) is homozygous across the whole of chromosome 5 on which the mating locus is situated. Analysis of whole-genome data, and confirmation by independent PCR and sequencing shows that this strain is homozygous for the a allele at the C. albicans mating locus and therefore could potentially mate with strains that are homozygous for the opposite mating type Whole-chromosome homozygosis is not an unusual mechanism by which natural strains of C. albicans become homozygous at the MTL locus (Hirakawa et al. 2015).

Most clinical strains of C. albicans belong to a small number of genetically diverged clades, have a global distribution and live alongside each other in the same human populations (Bougnoux et al. 2006; Odds et al. 2007). Phylogenetic comparisons between oak and clinical strains can be used to determine whether oak strains form distinct populations that differ genetically from clinical strains, as they do in S. cerevisiae (Almeida et al. 2015; Peter et al. 2018). Using whole-genome phylogenetic analysis, we therefore compared oak strains to clinical strains from 17 of the most abundant C. albicans clades (two or three strains from each clade) and 10 further strains that are from unknown clades [data from Ropars et al. (2018); Figure 2A].

All three oak strains are phylogenetically distinct from each other and more similar to clinical strains than they are to each other (Figure 2). One strain from oak (NCYC 4146) belongs to clade 4, which is one of the most abundant clades, with a known worldwide distribution (Figure 2). This clade assignment is also supported by the region of LOH that we see on the right arm of chromosome 3 (Figure 1A), which Ropars et al. (2018) showed was common to all clade 4 strains. Another oak strain (NCYC 4144) is similar to clade 18 strains (Figure 2), which have been isolated from east Asia and Portugal (Shin et al. 2011; Ropars et al. 2018). In contrast, the oak strain NCYC 4145 is unlike any of the 27 clinical lineages represented in our phylogenetic analysis (Figure 2). Genome data are only available for two strains of C. albicans from animals, and both were from starlings in France belonging to clade 16; none of the oak strains are similar to these (CEC3550 and CEC6000 in Figure 2A). Phylogenetic analysis of MLST loci also shows that oak strains are no more similar to 28 strains from wild and domesticated animals from the United States than they are to strains from humans (Figure S5).

By considering only whole-genome phylogenies, or data pooled across many loci, we could miss genetic similarities between the oak strain of unknown clade (NCYC 4145) and known clades. For example, if NCYC 4145 is a parasexual hybrid between two strains of known clade, its phylogenetic placement could suggest it is distinct from both parents. To detect regional genomic similarities, we therefore compared each oak strain genome to every other oak and clinical strain genome by painting their chromosomes in silico according to the clade assignment of similar strains (Figure 2B). This analysis of NCYC4145 in short (100 kb) blocks across the whole genome suggests that it is genetically diverged from all sampled clades (Figure 2B). Compared with other oak strains (Figure 2B) or with clinical strains from known clades (Figure S6, aq), NCYC4145 had more regions that were diverged from other sampled strains. In this, NCYC4145 is similar to clinical strains that are from clades only represented by a single strain (Figure S6r). Fine-scale chromosome painting analysis shows that the clade assignment of the other two oak strains are consistent across almost all parts of the genome (Figure 2B). As expected for a predominantly asexual species, we also see this consistency in clade assignment for all clinical strains of known clade (Figure S6, aq).

Levels of heterozygosity are high in C. albicans compared with the levels expected from a sexually reproducing species (Bougnoux et al. 2008), and this is likely to be the ancestral state for the species (Ropars et al. 2018). In the absence of mating and mitotic recombination, the haplotypes within a lineage will diverge as they accumulate mutations, whereas in sexual species, recombination can lead to increased similarity between alleles (Birky 1996; Halkett et al. 2005). Because heterozygosity correlates with fitness (Hickman et al. 2013; Hirakawa et al. 2015; Ciudad et al. 2016), virulence, and niche breadth (Ropars et al. 2018), we compared levels of heterozygosity between the three oak strain genomes and 180 of the clinical strain genomes analyzed by Ropars et al. (2018). High-quality sequence was available for 14 million sites in the genome for all oak and clinical strains, and we estimated the proportion of these sites that were heterozygous (Table 2 and Table S3). We excluded two clinical strains of C. albicans (CEC3678 and CEC3638 from clades 1 and 3) from the data set of Ropars et al. (2018) because these had fewer than 9 million high-quality sites.

Levels of heterozygosity are higher in the oak strains (0.61, 0.62, and 0.77%) than they are for 180 clinical strains (mean, 0.48%; Table 2; Wilcoxon test, ). In contrast, the clinical strain of C. albicans (NCYC 597) that we studied in the same sequencing batch as the oak strains showed a level of heterozygosity (0.48%) that was similar to other clinical strains (Table 2), suggesting that high heterozygosity is not an artifact of the sequencing methods used in this study. Furthermore, we excluded all sites with low quality sequence (with an expected error rate over 1 in 10,000), and the oak strains did not differ from clinical strains in the amount of high-quality sequence analyzed (Wilcoxon test, Table S3).

Levels of heterozygosity can vary within genomes because of recent LOH, and higher heterozygosity at centromeres that evolve faster than other genomic regions in C. albicans (Padmanabhan et al. 2008; Ropars et al. 2018). The number of heterozygous sites could also be overestimated in repetitive regions as a result of the mismapping of short reads to the reference genome. We therefore estimated levels of heterozygosity after filtering out LOH regions, centromeres, known repeats (using the reference genome annotation), and sites with over double the mean genome-wide read depth that could represent unannotated repeats. Even after applying this filter, levels of heterozygosity are higher for oak strains (mean, 0.70%) than they are for clinical strains (mean, 0.56%; Wilcoxon test, Table 2). This difference in heterozygosity results from heterozygosity at thousands of sites across the genome (Table S3). For example, the strain NCYC 4145 is heterozygous at 0.78% of the 11.4 million sites we studied after filtering, and therefore has 20,000 more heterozygous sites than expected for a clinical strain, and 5000 more heterozygous sites than expected for the most heterozygous of the 180 clinical strains (0.73% for CEC5026 from clade 9; Table S3).

There is recent evidence that C. albicans clades can differ in levels of heterozygosity (Ropars et al. 2018). For example, 35 of the 180 clinical strains are clade 13 strains, which are unusually homozygous compared with other clades (Ropars et al. 2018). We also observe substantial differences among the clades of clinical strains in levels of heterozygosity even after filtering LOH regions, centromeres, and repeats (ANOVA: ). Clade 13 strains are unusually homozygous (mean, 0.33%), compared to the average for clinical strains (mean, 0.56%), while clades 9, 10, and 16 are the most heterozygous. Could oak strains be highly heterozygous simply because they belong to highly heterozygous clades? ANOVA shows that oak strains are more heterozygous than clinical strains even when comparing them to strains with similar clade assignments (Table 2; ANOVA: ), and when excluding the homozygous clade 13 strains from the comparison (ANOVA: ). The oak strains NCYC 4146 and NCYC 4144 are more heterozygous than any other strain from their respective clades 4 and 18, while NCYC 4145, which we could not assign to a clade, was more heterozygous than any of the 180 clinical strains (Table 2).

The three oak strains might also differ from the sample of 180 clinical strains at their MTL locus (Table 2). The clinical strains show a ratio of genotypes at their MTL locus, therefore it is surprising to encounter an genotype in a sample of only three oak strains (Fishers exact test, ). To exclude the possibility that this difference could explain the higher levels of heterozygosity of oak strains, we also compared the oak strains to a sample of 22 clinical strains with an MTL genotype ratio that is more similar to that seen in oak, (Table S2; data from Hirakawa et al. 2015). Levels of heterozygosity are also higher for oak strains (0.610.77%) than for any of these 22 clinical strains (0.350.60%; Table S2; Wilcoxon test, ). Once more, after filtering out LOH regions, centromeres, and repeats, oak strains are more heterozygous (mean, 0.70%) than clinical strains (mean, 0.60%; Table S2; Wilcoxon test, ). Finally, to address the possibility that oak strains have undergone less LOH in fast-evolving regions than clinical strains, and that this could therefore account for their higher heterozygosity, we also measured heterozygosity at 948,860 nucleotide sites that were high-quality, non-LOH, nonrepetitive, and noncentromeric in all 22 oak and clinical strains from Table S2. At these sites, oak strains were more heterozygous (mean, 0.72%) than clinical strains (mean, 0.61%; Wilcoxon test, Table S2). In all analyses across multiple data sets, oak strains therefore show a small but statistically significant elevation in their levels of heterozygosity.

Phylogenetic analyses and fine-scale genome-wide DNA sequence comparisons show that all three strains from oaks from a single woodland site belong to distinct clades that show substantial genetic divergence (Figure 2). Two of the oak strains (NCYC 4146 and NCYC 4144) belong to clades 4 and 18, and both of these clades have been encountered in European clinical strains as well as from other continents (Odds et al. 2007; Shin et al. 2011), while one oak strain (NCYC 4145) is from a rare clade that has not yet been described. C. albicans strains from wild and domestic animals from Germany, northwestern Europe, and the United States show greater similarity to strains from humans than to each other, suggesting migration of C. albicans strains between humans and other animals (Edelmann et al. 2005; Jacobsen et al. 2008; Wrobel et al. 2008). Phylogenetic analysis at MLST loci also shows that the oak strains are no more similar to animal strains than they are to strains from humans [Figure S5; data from Wrobel et al. (2008)]. Our findings therefore suggest that migration between humans and woodland environments is also possible.

Could the oak strains represent a random set of recent migrants from humans to the oak environment? This possibility is difficult to reconcile with the different levels of heterozygosity seen in oak strains compared to 180 clinical strains (Table 2). The higher heterozygosity of oak strains remains when we account for the differences between clades (Table 2; ANOVA: ), and when we compare to a different set of 22 clinical strains with more MTL homozygous strains (mean, 0.60%; Table S2; Wilcoxon test, ). In other Candida species, high genome-wide heterozygosity has arisen as a result of hybridization between subspecies (Pryszcz et al. 2014). Chromosome-painting analysis shows that interclade hybridization is not the source of the high heterozygosity seen in C. albicans from oak (Figure 2B).

High levels of heterozygosity probably represent the ancestral state for C. albicans, because most closely related Candida species also show high levels of heterozygosity (Ropars et al. 2018), which is expected for asexual species (Birky 1996). Consistent with the idea that low heterozygosity represents the derived state for the species, strains from the most homozygous clade (clade 13) have sustained many loss-of-function mutations to their genes, grow poorly under a range of laboratory conditions, and have a restricted niche compared with other clades (Ropars et al. 2018). In C. albicans, there is also evidence that high heterozygosity is maintained through natural selection of heterozygotes that do not expose recessive deleterious mutations. Natural strains with high genome-wide heterozygosity show higher laboratory fitness (Hirakawa et al. 2015), while homozygous diploid strains grow poorly compared to heterozygous strains (Hickman et al. 2013) and LOH across even small genomic regions can lead to negative fitness consequences under stress (Ciudad et al. 2016). Therefore, the high genome-wide heterozygosity of C. albicans from oaks suggests that this is not necessarily a transient niche, and that these strains have not been subject to less natural selection than clinical strains.

The phenotypes of these oak strains also suggest that they have not narrowed their niche relative to clinical strains. Unlike the relatively homozygous clade 13 strains, which do not grow well at high temperature (42) and have only been isolated from the genital niche in humans (Ropars et al. 2018), the oak strains grew well at 42, suggesting that they would not be restricted to a superficial niche in mammals. Past studies of C. albicans from grass and shrubs showed that environmental isolates were able to grow in rabbits and kill them within days (van Uden et al. 1956; Di Menna 1958). We do, however, observe more phenotypic differences among oak strains (Table S1) than in these early studies (van Uden et al. 1956; Di Menna 1958). This functional diversity could reflect the differences in mating type, heterozygosity, or clade among oak strains.

C. albicans from oak differ from clinical strains in that they are unusually heterozygous, showing heterozygosity at thousands of sites more than expected for clinical strains (Table 2 and Table S3). Furthermore, the three oak strains were genetically diverged from each other (Figure 2), which implies that they do not represent laboratory contaminants from a human. Humans only rarely carry more than one distinct strain of C. albicans, and strains from multiple clades are especially rare (Bougnoux et al. 2006). In addition, these strains were isolated from three different trees that were more than 75 m apart, from bark over 1.5 m above the ground, and alongside negative controls that were clear (Robinson et al. 2016). The genetic divergence between oak strains also implies that these oak trees were not colonized as a result of migration from a single animal in the woods. It is rare for domestic or wild animals to carry multiple strains of C. albicans and it is especially rare for these to belong to different clades (Wrobel et al. 2008).

Experiments with S. cerevisiae and Saccharomyces paradoxus show that yeast can grow on the nutrients in oak bark (Kowallik et al. 2015) and live in forest soils for months or years (Anderson et al. 2018). C. tropicalis are also reliably isolated from trees in Canada over a period of several years (Carvalho et al. 2014). Intriguingly, C. albicans only occurred on some of the oldest oak trees compared with our European sample (Wilcoxon test, Robinson et al. 2016) or with other trees in the New Forest (Table 1). If oak C. albicans are merely recent migrants from animals, then they should occur on young and old trees with equal probability. In contrast, we expect a greater prevalence of C. albicans on old trees if they resemble other yeast species that colonize oak trees gradually and persist there over a period of decades (Robinson et al. 2016). Therefore, the occurrence of phylogenetically diverse C. albicans on unusually old oak trees suggests that it could live in this environment for decades, and that it is not an obligate commensal of warm-blooded animals.

If C. albicans can stably inhabit a woodland environment, then why have they only been isolated from trees on a handful occasions (Lachance et al. 2011; Robinson et al. 2016)? For example, three surveys of trees did not discover C. albicans but reported the isolation of other Candida species, and therefore could have detected C. albicans if it were present (Maganti et al. 2011; Charron et al. 2014; Sylvester et al. 2015). More recently, a larger survey did yield several C. albicans strains on fruit, soil, and plant matter in northern North America (Opulente et al. 2018), so the lack of C. albicans environmental isolates could be due to a lack of past sampling effort. In addition, if past surveys for woodland yeast did not target old trees, it is possible that C. albicans could have been missed.

The comparison between other human pathogenic fungi, such as Cryptococcus, and their wild relatives on trees is important for understanding disease emergence (Gerstein and Nielsen 2017). Furthermore, study of the natural enemies of C. gattii that occur where it resides on plants could lead to the development of new antifungal drugs (Mayer and Kronstad 2017). If C. albicans is not an obligate commensal of warm-blooded animals, then comparisons between clinical and free-living strains of C. albicans will also be important for understanding its commensalism and pathogenicity. A major limitation in this endeavor is that very few C. albicans strains are available for study from nonanimal sources. The few isolates that have been obtained were from a broad range of sources (van Uden et al. 1956; Di Menna 1958; Lachance et al. 2011; Robinson et al. 2016), and general environmental sampling for fungal pathogens can be challenging (Gerstein and Nielsen 2017). In the future, the targeting of old trees could lead to improved environmental sampling success.

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genetics – Dictionary Definition : Vocabulary.com

Genetics is the study of the traits people and other animals inherit from their family through DNA.

Compare the size of your nose to your father's and you are dealing with genetics but only if he's your biological father. Genetics involves studying genes DNA to look at how organisms evolve and are related. Scientists use genetics to prove whether genes for things like depression or intelligence exist. One of the most commonly discussed examples of genetics is what determines if a man will lose his hair: oddly, men inherit the baldness gene from their mothers, not their fathers.

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Welcome to the Department of Genetics

The mission of the Department of Genetics is to promote excellence in education and research in the areas of model organism genetics, human genetics, computational genetics, bioinformatics, and genomics. The Department is situated on the Busch Campus of Rutgers University in Piscataway, NJ. There are more than 30 faculty members in the Department, with laboratories located in the Nelson Biological Laboratories, the Life Sciences Building, and the Waksman Institute.

The Department is affiliated with the Human Genetics Institute of New Jersey (HGINJ), which houses core microscopy and imaging facilities and offers state-of-the-art custom genomic solutions through RUCDR Infinite Biologics. As the world's largest university-based biorepository, RUCDR provides comprehensive services in bioprocessing, genomics, sample analytics and biostorage to the global scientific community. The Department oversees an undergraduate major in genetics within the Division of Life Science (DLS) and the Schools of Arts and Sciences (SAS), and the Genetic Counseling Master's Program.

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Human genetics | biology | Britannica.com

Human genetics, study of the inheritance of characteristics by children from parents. Inheritance in humans does not differ in any fundamental way from that in other organisms.

The study of human heredity occupies a central position in genetics. Much of this interest stems from a basic desire to know who humans are and why they are as they are. At a more practical level, an understanding of human heredity is of critical importance in the prediction, diagnosis, and treatment of diseases that have a genetic component. The quest to determine the genetic basis of human health has given rise to the field of medical genetics. In general, medicine has given focus and purpose to human genetics, so the terms medical genetics and human genetics are often considered synonymous.

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genetics: Human genetics

Some geneticists specialize in the hereditary processes of human genetics. Most of the emphasis is on understanding and treating genetic disease and genetically influenced ill health, areas collectively known as medical genetics. One broad area of activity is laboratory research dealing with the

A new era in cytogenetics, the field of investigation concerned with studies of the chromosomes, began in 1956 with the discovery by Jo Hin Tjio and Albert Levan that human somatic cells contain 23 pairs of chromosomes. Since that time the field has advanced with amazing rapidity and has demonstrated that human chromosome aberrations rank as major causes of fetal death and of tragic human diseases, many of which are accompanied by mental retardation. Since the chromosomes can be delineated only during mitosis, it is necessary to examine material in which there are many dividing cells. This can usually be accomplished by culturing cells from the blood or skin, since only the bone marrow cells (not readily sampled except during serious bone marrow disease such as leukemia) have sufficient mitoses in the absence of artificial culture. After growth, the cells are fixed on slides and then stained with a variety of DNA-specific stains that permit the delineation and identification of the chromosomes. The Denver system of chromosome classification, established in 1959, identified the chromosomes by their length and the position of the centromeres. Since then the method has been improved by the use of special staining techniques that impart unique light and dark bands to each chromosome. These bands permit the identification of chromosomal regions that are duplicated, missing, or transposed to other chromosomes.

Micrographs showing the karyotypes (i.e., the physical appearance of the chromosome) of a male and a female have been produced. In a typical micrograph the 46 human chromosomes (the diploid number) are arranged in homologous pairs, each consisting of one maternally derived and one paternally derived member. The chromosomes are all numbered except for the X and the Y chromosomes, which are the sex chromosomes. In humans, as in all mammals, the normal female has two X chromosomes and the normal male has one X chromosome and one Y chromosome. The female is thus the homogametic sex, as all her gametes normally have one X chromosome. The male is heterogametic, as he produces two types of gametesone type containing an X chromosome and the other containing a Y chromosome. There is good evidence that the Y chromosome in humans, unlike that in Drosophila, is necessary (but not sufficient) for maleness.

A human individual arises through the union of two cells, an egg from the mother and a sperm from the father. Human egg cells are barely visible to the naked eye. They are shed, usually one at a time, from the ovary into the oviducts (fallopian tubes), through which they pass into the uterus. Fertilization, the penetration of an egg by a sperm, occurs in the oviducts. This is the main event of sexual reproduction and determines the genetic constitution of the new individual.

Human sex determination is a genetic process that depends basically on the presence of the Y chromosome in the fertilized egg. This chromosome stimulates a change in the undifferentiated gonad into that of the male (a testicle). The gonadal action of the Y chromosome is mediated by a gene located near the centromere; this gene codes for the production of a cell surface molecule called the H-Y antigen. Further development of the anatomic structures, both internal and external, that are associated with maleness is controlled by hormones produced by the testicle. The sex of an individual can be thought of in three different contexts: chromosomal sex, gonadal sex, and anatomic sex. Discrepancies between these, especially the latter two, result in the development of individuals with ambiguous sex, often called hermaphrodites. The phenomenon of homosexuality is of uncertain cause and is unrelated to the above sex-determining factors. It is of interest that in the absence of a male gonad (testicle) the internal and external sex anatomy is always female, even in the absence of a female ovary. A female without ovaries will, of course, be infertile and will not experience any of the female developmental changes normally associated with puberty. Such a female will often have Turners syndrome.

If X-containing and Y-containing sperm are produced in equal numbers, then according to simple chance one would expect the sex ratio at conception (fertilization) to be half boys and half girls, or 1 : 1. Direct observation of sex ratios among newly fertilized human eggs is not yet feasible, and sex-ratio data are usually collected at the time of birth. In almost all human populations of newborns, there is a slight excess of males; about 106 boys are born for every100 girls. Throughout life, however, there is a slightly greater mortality of males; this slowly alters the sex ratio until, beyond the age of about 50 years, there is an excess of females. Studies indicate that male embryos suffer a relatively greater degree of prenatal mortality, so the sex ratio at conception might be expected to favour males even more than the 106 : 100 ratio observed at birth would suggest. Firm explanations for the apparent excess of male conceptions have not been established; it is possible that Y-containing sperm survive better within the female reproductive tract, or they may be a little more successful in reaching the egg in order to fertilize it. In any case, the sex differences are small, the statistical expectation for a boy (or girl) at any single birth still being close to one out of two.

During gestationthe period of nine months between fertilization and the birth of the infanta remarkable series of developmental changes occur. Through the process of mitosis, the total number of cells changes from 1 (the fertilized egg) to about 2 1011. In addition, these cells differentiate into hundreds of different types with specific functions (liver cells, nerve cells, muscle cells, etc.). A multitude of regulatory processes, both genetically and environmentally controlled, accomplish this differentiation. Elucidation of the exquisite timing of these processes remains one of the great challenges of human biology.

Immunity is the ability of an individual to recognize the self molecules that make up ones own body and to distinguish them from such nonself molecules as those found in infectious microorganisms and toxins. This process has a prominent genetic component. Knowledge of the genetic and molecular basis of the mammalian immune system has increased in parallel with the explosive advances made in somatic cell and molecular genetics.

There are two major components of the immune system, both originating from the same precursor stem cells. The bursa component provides B lymphocytes, a class of white blood cells that, when appropriately stimulated, differentiate into plasma cells. These latter cells produce circulating soluble proteins called antibodies or immunoglobulins. Antibodies are produced in response to substances called antigens, most of which are foreign proteins or polysaccharides. An antibody molecule can recognize a specific antigen, combine with it, and initiate its destruction. This so-called humoral immunity is accomplished through a complicated series of interactions with other molecules and cells; some of these interactions are mediated by another group of lymphocytes, the T lymphocytes, which are derived from the thymus gland. Once a B lymphocyte has been exposed to a specific antigen, it remembers the contact so that future exposure will cause an accelerated and magnified immune reaction. This is a manifestation of what has been called immunological memory.

The thymus component of the immune system centres on the thymus-derived T lymphocytes. In addition to regulating the B cells in producing humoral immunity, the T cells also directly attack cells that display foreign antigens. This process, called cellular immunity, is of great importance in protecting the body against a variety of viruses as well as cancer cells. Cellular immunity is also the chief cause of the rejection of organ transplants. The T lymphocytes provide a complex network consisting of a series of helper cells (which are antigen-specific), amplifier cells, suppressor cells, and cytotoxic (killer) cells, all of which are important in immune regulation.

One of the central problems in understanding the genetics of the immune system has been in explaining the genetic regulation of antibody production. Immunobiologists have demonstrated that the system can produce well over one million specific antibodies, each corresponding to a particular antigen. It would be difficult to envisage that each antibody is encoded by a separate gene; such an arrangement would require a disproportionate share of the entire human genome. Recombinant DNA analysis has illuminated the mechanisms by which a limited number of immunoglobulin genes can encode this vast number of antibodies.

Each antibody molecule consists of several different polypeptide chainsthe light chains (L) and the longer heavy chains (H). The latter determine to which of five different classes (IgM, IgG, IgA, IgD, or IgE) an immunoglobulin belongs. Both the L and H chains are unique among proteins in that they contain constant and variable parts. The constant parts have relatively identical amino acid sequences in any given antibody. The variable parts, on the other hand, have different amino acid sequences in each antibody molecule. It is the variable parts, then, that determine the specificity of the antibody.

Recombinant DNA studies of immunoglobulin genes in mice have revealed that the light-chain genes are encoded in four separate parts in germ-line DNA: a leader segment (L), a variable segment (V), a joining segment (J), and a constant segment (C). These segments are widely separated in the DNA of an embryonic cell, but in a mature B lymphocyte they are found in relative proximity (albeit separated by introns). The mouse has more than 200 light-chain variable region genes, only one of which will be incorporated into the proximal sequence that codes for the antibody production in a given B lymphocyte. Antibody diversity is greatly enhanced by this system, as the V and J segments rearrange and assort randomly in each B-lymphocyte precursor cell. The mechanisms by which this DNA rearrangement takes place are not clear, but transposons are undoubtedly involved. Similar combinatorial processes take place in the genes that code for the heavy chains; furthermore, both the light-chain and heavy-chain genes can undergo somatic mutations to create new antibody-coding sequences. The net effect of these combinatorial and mutational processes enables the coding of millions of specific antibody molecules from a limited number of genes. It should be stressed, however, that each B lymphocyte can produce only one antibody. It is the B lymphocyte population as a whole that produces the tremendous variety of antibodies in humans and other mammals.

Plasma cell tumours (myelomas) have made it possible to study individual antibodies, since these tumours, which are descendants of a single plasma cell, produce one antibody in abundance. Another method of obtaining large amounts of a specific antibody is by fusing a B lymphocyte with a rapidly growing cancer cell. The resultant hybrid cell, known as a hybridoma, multiplies rapidly in culture. Since the antibodies obtained from hybridomas are produced by clones derived from a single lymphocyte, they are called monoclonal antibodies.

As has been stated, cellular immunity is mediated by T lymphocytes that can recognize infected body cells, cancer cells, and the cells of a foreign transplant. The control of cellular immune reactions is provided by a linked group of genes, known as the major histocompatibility complex (MHC). These genes code for the major histocompatibility antigens, which are found on the surface of almost all nucleated somatic cells. The major histocompatibility antigens were first discovered on the leukocytes (white blood cells) and are therefore usually referred to as the HLA (human leukocyte group A) antigens.

The advent of the transplantation of human organs in the 1950s made the question of tissue compatibility between donor and recipient of vital importance, and it was in this context that the HLA antigens and the MHC were elucidated. Investigators found that the MHC resides on the short arm of chromosome 6, on four closely associated sites designated HLA-A, HLA-B, HLA-C, and HLA-D. Each locus is highly polymorphic; i.e., each is represented by a great many alleles within the human gene pool. These alleles, like those of the ABO blood group system, are expressed in codominant fashion. Because of the large number of alleles at each HLA locus, there is an extremely low probability of any two individuals (other than siblings) having identical HLA genotypes. (Since a person inherits one chromosome 6 from each parent, siblings have a 25 percent probability of having received the same paternal and maternal chromosomes 6 and thus of being HLA matched.)

Although HLA antigens are largely responsible for the rejection of organ transplants, it is obvious that the MHC did not evolve to prevent the transfer of organs from one person to another. Indeed, information obtained from the histocompatibility complex in the mouse (which is very similar in its genetic organization to that of the human) suggests that a primary function of the HLA antigens is to regulate the number of specific cytotoxic T killer cells, which have the ability to destroy virus-infected cells and cancer cells.

More is known about the genetics of the blood than about any other human tissue. One reason for this is that blood samples can be easily secured and subjected to biochemical analysis without harm or major discomfort to the person being tested. Perhaps a more cogent reason is that many chemical properties of human blood display relatively simple patterns of inheritance.

Certain chemical substances within the red blood cells (such as the ABO and MN substances noted above) may serve as antigens. When cells that contain specific antigens are introduced into the body of an experimental animal such as a rabbit, the animal responds by producing antibodies in its own blood.

In addition to the ABO and MN systems, geneticists have identified about 14 blood-type gene systems associated with other chromosomal locations. The best known of these is the Rh system. The Rh antigens are of particular importance in human medicine. Curiously, however, their existence was discovered in monkeys. When blood from the rhesus monkey (hence the designation Rh) is injected into rabbits, the rabbits produce so-called Rh antibodies that will agglutinate not only the red blood cells of the monkey but the cells of a large proportion of human beings as well. Some people (Rh-negative individuals), however, lack the Rh antigen; the proportion of such persons varies from one human population to another. Akin to data concerning the ABO system, the evidence for Rh genes indicates that only a single chromosome locus (called r) is involved and is located on chromosome 1. At least 35 Rh alleles are known for the r location; basically the Rh-negative condition is recessive.

A medical problem may arise when a woman who is Rh-negative carries a fetus that is Rh-positive. The first such child may have no difficulty, but later similar pregnancies may produce severely anemic newborn infants. Exposure to the red blood cells of the first Rh-positive fetus appears to immunize the Rh-negative mother, that is, she develops antibodies that may produce permanent (sometimes fatal) brain damage in any subsequent Rh-positive fetus. Damage arises from the scarcity of oxygen reaching the fetal brain because of the severe destruction of red blood cells. Measures are available for avoiding the severe effects of Rh incompatibility by transfusions to the fetus within the uterus; however, genetic counselling before conception is helpful so that the mother can receive Rh immunoglobulin immediately after her first and any subsequent pregnancies involving an Rh-positive fetus. This immunoglobulin effectively destroys the fetal red blood cells before the mothers immune system is stimulated. The mother thus avoids becoming actively immunized against the Rh antigen and will not produce antibodies that could attack the red blood cells of a future Rh-positive fetus.

Human serum, the fluid portion of the blood that remains after clotting, contains various proteins that have been shown to be under genetic control. Study of genetic influences has flourished since the development of precise methods for separating and identifying serum proteins. These move at different rates under the impetus of an electrical field (electrophoresis), as do proteins from many other sources (e.g., muscle or nerve). Since the composition of a protein is specified by the structure of its corresponding gene, biochemical studies based on electrophoresis permit direct study of tissue substances that are only a metabolic step or two away from the genes themselves.

Electrophoretic studies have revealed that at least one-third of the human serum proteins occur in variant forms. Many of the serum proteins are polymorphic, occurring as two or more variants with a frequency of not less than 1 percent each in a population. Patterns of polymorphic serum protein variants have been used to determine whether twins are identical (as in assessing compatibility for organ transplants) or whether two individuals are related (as in resolving paternity suits). Whether the different forms have a selective advantage is not generally known.

Much attention in the genetics of substances in the blood has been centred on serum proteins called haptoglobins, transferrins (which transport iron), and gamma globulins (a number of which are known to immunize against infectious diseases). Haptoglobins appear to relate to two common alleles at a single chromosome locus; the mode of inheritance of the other two seems more complicated, about 18 kinds of transferrins having been described. Like blood-cell antigen genes, serum-protein genes are distributed worldwide in the human population in a way that permits their use in tracing the origin and migration of different groups of people.

Hundreds of variants of hemoglobin have been identified by electrophoresis, but relatively few are frequent enough to be called polymorphisms. Of the polymorphisms, the alleles for sickle-cell and thalassemia hemoglobins produce serious disease in homozygotes, whereas others (hemoglobins C, D, and E) do not. The sickle-cell polymorphism confers a selective advantage on the heterozygote living in a malarial environment; the thalassemia polymorphism provides a similar advantage.

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Human genetics | biology | Britannica.com